Suprasellar cyst presenting with bobble-head doll syndrome

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Authors

George, Roshan
Gaxa, Luvo
Lockhat, Zarina I.
Hlahla, Stevens Kgomotso
Van der Meyden, Cornelis Hendrikus
Kisten, Ravendran
Bida, Nndweleni Meshack

Journal Title

Journal ISSN

Volume Title

Publisher

Elsevier

Abstract

BACKGROUND : Bobble-head doll syndrome is a rare neurological syndrome presenting with repetitive anteroposterior head movements. It is usually associated with expansile cystic lesions in the third ventricular region. CASE DESCRIPTION : An 8-year-old boy presented with involuntary bobbling head movements. Magnetic resonance imaging of the brain revealed an extensive suprasellar cyst resulting in obstructive hydrocephalus. Endoscopic ventriculo-cysto-cisternostomy resulted in improved clinical outcome. CONCLUSIONS : Endoscopic ventriculo-cysto-cisternostomy is an effective, less-invasive technique in the treatment of suprasellar cysts that results in resolution of the bobbling head movements.

Description

Supplementary Data: Video 1. Video demonstrating bobbling head movements prior to surgery.
Video 2. Video demonstrating significant improvement of bobbling head movements post surgery.

Keywords

Arachnoid cyst, Bobble-head doll syndrome (BHDS), Head bobbing, Suprasellar cyst, Children, Neurological syndrome

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Citation

George, R., Gaxa, L., Lockhat, Z. et al. 2020, 'Suprasellar cyst presenting with bobble-head doll syndrome', World Neurosurgery, vol. 133, pp. 80-83.